WPW syndrome

Pediatrics & Emergencies

Prevalence

Epidemiology of the Wolff-Parkinson-White pattern and syndrome.

1-3 per 1,000
population
2:1 Relationship
Men: Women

Pattern vs. Syndrome

He pattern WPW are ECG findings without symptoms (silent accessory pathway). He syndrome WPW is the presence of the electrocardiographic pattern accompanied by symptomatic tachyarrhythmias.

Presentation Peak

Although it is congenital, it usually manifests in the childhood and adolescence. Up to 20-30% of children diagnosed in infancy may lose conduction through the accessory pathway spontaneously as they grow older.

Clinical Presentation

Signs in Infants

Infants cannot report palpitations. Diagnosis in the emergency room requires high clinical suspicion in the face of non-specific symptoms.

  • Extreme irritability or lethargy
  • Feeding refusal / Poor suction
  • Paleness or cyanosis
  • Tachypnea and heart failure
  • HR is usually > 220-250 bpm

Older Children and Adolescents

sudden palpitations
Dyspnea or chest pain
Dizziness/Presyncope
Syncope (Alarm sign)

ECG (Sinus Rhythm) Criteria

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Management in Emergencies

Hemodynamic Instability?

Hypotension, sensory disturbance, shock, severe heart failure.

Synchronized Electrical Cardioversion (0.5 - 1 J/kg)

Stable Patient (SVT - TRIN or Orthodromic)

1

Vagal Maneuvers

Infants: Ice on the face (immersion reflex) for 10-15 seconds.
Older children: Modified Valsalva maneuver, blowing through a straw or syringe.

2

Pharmacological Treatment

Adenosine (Rapid IV/IO Bolus)

Initial dose: 0.1 mg/kg (max 6 mg).
Second dose: 0.2 mg/kg (max 12 mg).
Always follow with SSF quick wash.

Absolute Contraindications

If the patient presents Pre-excited Atrial Fibrillation (irregular wide QRS tachycardia), blocking the AV node is lethal. All conduction will pass through the accessory pathway, degenerating into Ventricular Fibrillation.

Avoid the "ABCD" rule:

  • Adenosine
  • Beta-blockers
  • Calkyoantagonists
  • DIgoxin / Diltiazem

Management in pre-excited AF: Procainamide, Amiodarone or Electrical Cardioversion.

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